Behcets disease

Diagnosis: Behcets disease

Behcets disease

Clinical Presentation

Behcets disease

Clinical History

Submitted by Ellie Goulding MD. Originally posted January 23, 2017.

Treatment

See case discussion.

Differential Diagnosis

• Herpes simplex • Aphthous stomatitis • Crohn disease • Reactive arthritis • SLE • Sweet syndrome • Syphilis

Key Learnings

• Systemic vasculitis affecting arteries and veins of all sizes • Classic triad: recurrent oral ulcers, genital ulcers, ocular inflammation (uveitis) • Pathergy test: sterile pustule 24-48h after needle prick — pathognomonic (especially in endemic populations) • Silk Road disease: Turkey, Iran, Japan, Korea — HLA-B51 association • Oral ulcers are required for diagnosis (International Study Group criteria) • Most feared complication: ocular disease → blindness if untreated

Tags: behcets, disease, ellie goulding md